Journal: JIMD Reports

Article Title: Diurnal variability of glucose tetrasaccharide (Glc 4 ) excretion in patients with glycogen storage disease type III

doi: 10.1002/jmd2.12181

Figure Lengend Snippet: Summary of diurnal variability of Glc 4 excretion in subjects with GSD III

Article Snippet: Acquity UPLC BEH amide 2.1 × 100 mm column, VanGuard guard column, and Sep‐Pak Vac C18 cartridges were obtained from Waters (Milford, Massachusetts), Glc 4 from Toronto Research Chemicals (Toronto, Canada), glacial acetic acid, butyl‐4‐aminobenzoate, sodium cyanoborohydride from Sigma (St. Louis, MO), and methanol and acetonitrile (HPLC grade) from VWR Scientific products (Atlanta, Georgia).

Techniques:

Journal: JIMD Reports

Article Title: Diurnal variability of glucose tetrasaccharide (Glc 4 ) excretion in patients with glycogen storage disease type III

doi: 10.1002/jmd2.12181

Figure Lengend Snippet: Comparison of the degree and variability of Glc 4 excretion with uncooked cornstarch dose. A, Glc 4 concentrations in 24‐hour urine relative to total cornstarch dose. No significant correlation was observed (Pearson R = −.349, P = .15, n = 18 patients). B, Variability (CV%) in Glc 4 excretion in 24‐hour urine relative to cornstarch dose. No significant correlation was observed (Pearson R = −.278, P = .15, n = 28 collections by 15 subjects)

Article Snippet: Acquity UPLC BEH amide 2.1 × 100 mm column, VanGuard guard column, and Sep‐Pak Vac C18 cartridges were obtained from Waters (Milford, Massachusetts), Glc 4 from Toronto Research Chemicals (Toronto, Canada), glacial acetic acid, butyl‐4‐aminobenzoate, sodium cyanoborohydride from Sigma (St. Louis, MO), and methanol and acetonitrile (HPLC grade) from VWR Scientific products (Atlanta, Georgia).

Techniques: